Ref. No Publication No Abstract Title Presenter
132 OP-01 A WEB-BASED COLLECTION OF GENOTYPE-PHENOTYPE CORRELATIONS IN HEREDITARY PERIODIC FEVERS FROM THE EUROFEVER REGISTRY (English) Riccardo Papa
11 OP-02 Efficacy and Safety of Canakinumab in Patients With HIDS/MKD: Results From the Pivotal Phase 3 CLUSTER Trial (English) Joost Frenkel
153 OP-03 Combination of clinical parameters and biomarkers for the prediction of colchicine dose increase in patients with FMF (English) Anne-Marie Knieper
25 OP-04 Comparison of patients with FMF accompanied with sacroiliitis and patients with enthesitis-related arthritis (English) Hafize Emine Sönmez
133 OP-05 A novel PAAND variant further defines 14-3-3 binding of Pyrin and distinction to FMF. (English) Fiona Moghaddas
72 OP-06 Possible role of microRNA-20a and microRNA-197 in Familial Mediterranean fever pathogenesis (English) Yeliz Z. Akkaya Ulum
221 OP-07 Gene mosaicism in autoinflammatory diseases – a Spanish centre experience (English) Anna Mensa-Vilaro
253 OP-08 Serum amyloid A and C-reactive protein in familial Mediterranean fever (English) HURİ ÖZDOĞAN
124 OP-09 HOMOZYGOUS MUTATION IN THE USP43 GENE MIGHT BE ASSOCIATED WITH A NEW TYPE OF INTERFERONOPATHY (English) Anna Kozlova
38 OP-10 A novel homozygote TREX1 mutation in two siblings, with different phenotypic effects: chilblains and cerebral vasculitis (English) Miray Kisla Ekinci
232 OP-11 The Deficiency of Adenosine Deaminase 2 (DADA2)–Results of Anti-TNF Treatment in Patients with a History of Stroke (English) Amanda Kilker Ombrello
214 OP-12 Use of Anticoagulants and Antiplatelets in Strokes Caused by Adenosine Deaminase Deficiency: A 22 Patient Analysis (English) Patrycja Hoffmann
130 OP-13 Therapeutic discontinuation of IL-1 inhibitors in CAPS, TRAPS, FMF and MKD: data from the JIRcohorte (English) Véronique Hentgen
236 OP-14 A New Auto-inflammatory Syndrome Caused by Mutations in RIPK1 that Prevent Its Cleavage by Caspase 8 (English) Deborah Stone
48 OP-15 An extracellular ionic milieu renders human granulocytic S100A12 into a pro-inflammatory TLR4-binding alarmin (English) Dirk Foell
139 OP-16 Mutations in the Tyrosine-Protein Kinase Lyn Cause an Early-Onset Neutrophilic Vasculitis Syndrome (English) Gina Montealegre
69 OP-17 INCREASED CIRCULATING ENDOTHELIAL MICROPARTICLES IN CHILDREN WITH FMF (English) Sibel Yel
8 OP-18 Efficacy and Safety of Canakinumab in Patients With TRAPS: Results From the Pivotal Phase 3 CLUSTER Trial (English) Marco Gattorno
7 OP-19 Efficacy and Safety of Canakinumab in Patients With Colchicine-Resistant FMF: Results From the Phase 3 CLUSTER Trial (English) Ahmet Gül
161 OP-20 Molecular genetic investigation, clinical features and response to treatment in 18 patients with Schnitzler’s syndrome (English) Dorota Rowczenio
63 OP-21 International experience of pregnancy outcomes in auto-inflammatory syndromes treated with Interleukin-1 inhibitors (English) Taryn Youngstein
93 OP-22 PFAPA syndrome in large pediatric population: a single center experience. (English) Ozgur Kasapcopur
36 OP-23 Dosing of Canakinumab in Patients With Still’s disease: Exposure-Response Analysis of Pooled SJIA Data by Age Groups (English) Paolo Sfriso
77 OP-24 Proteomic profile of patients with different autoinflammatory diseases: an approach to identify new biomarkers (English) Federica Penco
112 OP-25 A novel autoinflammatory disease due to homozygous MEFV Mutations affecting the S208 domain of the pyrin protein (English) ying hong
55 OP-26 IFN-GAMMA (IFNγ), IFNγ-INDUCED CHEMOKINES AND OTHER BIOMARKERS IN MACROPHAGE ACTIVATION SYNDROME (MAS) (English) Claudia Bracaglia
44 OP-27 Consensus-based diagnostic approach to systemic juvenile idiopathic arthritis in Germany (English) Dirk Foell
125 OP-28 Novel immune and inflammatory loci associated with Behçet’s disease. (English) Elaine F Remmers
95 OP-29 Developing Consensus Treatment Plans for PFAPA: A Preliminary Effort from the CARRA PFAPA Subcommittee (English) Gil Amarilyo
53 OP-30 Mosaic mutation detection using single molecule molecular inversion probes (smMIPs) for autoinflammatory disorders (English) Ellen Carbo
230 OP-31 NGS panel in routine for autoinflammatory diseases: updating the experience of Montpellier (English) Guillaume Sarrabay
59 OP-32 Adipocyte production of inflammatory cytokines may be contributory in cases of AA Amyloidosis of unknown aetiology (English) Taryn Youngstein
28 OP-33 A 15-year, single centre experience of anakinra in 205 patients with systemic autoinflammatory disorders (English) Thirusha Lane
254 OP-34 Heat Intolerance in FMF– a preliminary report of an intriguing association and its potential implications Avi Livneh
75 PP-01 Validation of MRP8/14 as diagnostic biomarker for systemic juvenile idiopathic arthritis in fever of unknown origin (English) Dirk Foell
165 PP-02 Problems in the diagnosis of Familial Mediterranean Fever in Turkey (English) Mustafa Erdoğan
32 PP-03 Evaluation of High Mobility Group Box 1 Protein as an Inflamation Marker in Patients with Familial Mediterranean Fever (English) Betül Öztürk
54 PP-04 Improving autoinflammatory diagnostics by sharing genetic variant classifications (English) Ellen Carbo
56 PP-05 NEXT GENERATION SEQUENCING (NGS) ANALYSIS OF FAMILIAL HLH RELATED GENES IN MAS AND SECONDARY HLH (secHLH) (English) Claudia Bracaglia
120 PP-06 An Update on the Diagnostics of Deficiency of ADA2 (DADA2) (English) Qing Zhou
142 PP-07 IL-1 Inhibition in Cryopyrin-Associated Periodic Syndrome – A 15-Year, Single-Centre Experience of Safety and Efficacy (English) Thirusha Lane
167 PP-08 Familial recurrent leukocytoclastic vasculitis associated with a novel mutation in NLRP12 (English) Fatma Dedeoglu
196 PP-09 Through new classification criteria for inherited periodic fevers.An integrated approach among clinicians and geneticist (English) Silvia Federici
208 PP-10 Genetic Analysis of Inherited Autoinflammatory Disorders (English) Ilker Karacan
212 PP-11 Local and systemic reaction to meningococcal vaccination in a patient with Cryopyrin-associated Periodic Syndrome (English) Jasmin Beate Kuemmerle-Deschner
156 PP-12 Identification of pathogenic variants in MVK and TNFRSF1A genes in MEFV negative families with FMF-like disease (English) Ilker Karacan
14 PP-13 MEFV MUTATIONS IN PATIENTS WITH GLOMERULONEPHRITIS: INCREASED CARRIER RATE AND IMPLICATIONS ON RENAL ENDPOINTS (English) Ufuk İlgen
30 PP-14 ASSESSMENT OF SUBCLINICAL INFLAMMATION IN CHILDREN WITH MEFV MUTATION AND FMF PATIENTS IN REMISSION (English) Ayşenur Paç Kısaarslan
35 PP-15 Neutrophil extracellular trap formation in Schnitzler’s syndrome (English) Hanna Bonnekoh
51 PP-16 Impaired sleep quality is associated with decreased quality of life in children with familial Mediterranean fever (English) Balahan Makay
62 PP-17 Adult-Onset Refractory Haemophagocytosis as the Presenting feature of TRAPS (English) Taryn Youngstein
81 PP-18 The Feverprints App: Crowdsourcing Technology to Study Temperatures in Health and Disease (English) Jonathan Samuel Hausmann
84 PP-19 NEXT-GENERATION SEQUENCING CONTRIBUTION FOR MOLEDCULAR DIAGNOSIS OF AUTOINFLAMMATORY DISEASES (English) Antonella Insalaco
94 PP-20 Anti-TNF therapy would be life-saving for DADA2 patients (English) Ozgur Kasapcopur
101 PP-21 Screening of Fabry disease in children with familial Mediterranean fever (English) Seçil Arslansoyu Çamlar
108 PP-22 Changes in quality of life in adult patients receiving anti-IL-1 therapies for TRAPS (English) Thirusha Lane
118 PP-23 Deficiency of CD70 is responsible of a case of chronic active EBV (CAEBV) infection presenting as periodic fever (English) Roberta Caorsi
126 PP-24 LACC1 Mutations in Familial Form of Juvenile Idiopathic Arthritis (English) Ilker Karacan
127 PP-25 EFFICACY AND SAFETY OF INTERLEUKIN-1 INHIBITORS IN FAMILIAL MEDITERRANEAN FEVER PATIENTS COMPLICATED WITH AMYLOIDOSIS (English) özkan varan
129 PP-26 Underlying Causes of Persistently Elevated Acute Phase Reactans in Patients wih Familial Mediternian Fever (English) özkan varan
145 PP-27 Mutant IKAROS causes impaired CD22 expression in peripheral B cells leading to disordered activation and early-onset SLE (English) Erika Van Nieuwenhove
152 PP-28 Canakinumab-treatment in autoinflammatory disease patients younger than 2 years old (English) betul sozeri
162 PP-29 Atypical FMF associated with multiple MEFV gene mutations in six patients from the Middle East. (English) Dorota Rowczenio
180 PP-30 Canakinumab experience from a pediatric rheumatology center in Istanbul (English) Mustafa Çakan
217 PP-31 RELATIONSHIP BETWEEN MENSTRUATION AND SYMPTOMS OF BEHÇET’S SYNDROME (English) Gul Guzelant
219 PP-32 An update on the Italian cohort of DADA2 patients and an assessment of a novel functional screening test (English) Roberta Caorsi
239 PP-33 AN EASY METHOD FOR TRACKING ATTACK DATA OF AUTOINFLAMMATORY DISEASES: AUTOINFLAMMATORY DISEASE DIARY (AIDD) APPLICATION (English) Abdurrahman Tufan
241 PP-34 Ustekinumab as effective treatment in DITRA syndrome (English) Roberta Caorsi
245 PP-35 SERUM CYTOKINE PROFILE IN BEHÇET’S DISEASE PATIENTS WITH MUCOCUTANEOUS AND OCULAR INVOLVEMENT (English) Giuseppe Lopalco
98 PP-36 ANTI-IL 1 TREATMENT IN 33 PEDIATRIC PATIENTS WITH FAMILIAL MEDITERRANEAN FEVER (English) Semanur Ozdel
99 PP-37 FATIGUE IN PEDIATRIC PATIENTS WITH FAMILIAL MEDITERRANEAN FEVER (English) Semanur Ozdel
151 PP-38 The characteristics of Familial Mediterranean Fever Patients with disease onset at before the age of two years (English) betul sozeri
166 PP-39 Characteristic of the familial Mediterranean fever patients presented with musculoskeletal findings (English) betul sozeri
204 PP-40 Evaluation of macrophage activation syndrome in systemic onset juvenile idiopathic arthritis according to 2016 criteria (English) Fatma Dedeoglu
18 PP-41 Molecular analysis of MEFV gene mutations in juvenile systemic lupus erythematosus and the role of disease severity (English) Serife Gul Karadag
22 PP-42 A First-in-Human Study to Evaluate the Safety, Tolerability, Pharmacokinetics and Pharmacodynamics of a Novel Anti-interleukin 1 Biologic Agent, RPH-104, in Healthy Subjects (English) Ahmet Gül
34 PP-43 Mucocutaneous Lesions and Recurrent Fevers in Patients with Trisomy 8 Mosaicism and Chromosome 8 Duplication (English) Kalpana Manthiram
37 PP-44 Intracellular detection of inflammatory cytokines in a differential diagnosis of autoinflammatory diseases (English) Anna Sediva
40 PP-45 VITAMIN B12 LEVELS IN PEDIATRIC FAMILIAL MEDITERRANEAN FEVER PATIENTS ON COLCHİCİNE TREATMENT (English) Ozge Başaran
58 PP-46 Cystic fibrosis an autoinflammatory disease-inflammasome activation in bronchial epithelial cells exacerbated by hypoxia (English) Michael McDermott
68 PP-47 Oral findings in children with Familial Mediterranean fever (FMF) (English) Pelin Esmeray
74 PP-48 Defect of adaptive immunity in ADA2 Deficiency patients (English) FRANCESCA SCHENA
76 PP-49 PFAPA syndrome is associated with a CARD8 variant unable to bind the NLRP3 inflammasome. (English) Katerina Theodoropoulou
78 PP-50 Characterization of CAPS KI mouse model to exploit new therapeutic approaches for the modulation of NLRP3 inflammasome. (English) Arinna Bertoni
88 PP-51 Colchicine Efficacy for Undefined Autoinflammatory Diseases (English) Jonathan Samuel Hausmann
97 PP-52 Assessment of Systemic Vascular Involvement in Children with Uveitis (English) seçil conkar
109 PP-53 Use of biologics to treat systemic autoinflammatory disorders in patients aged over 70 years (English) Thirusha Lane
111 PP-54 Clinical impact of a targeted next-generation sequencing gene panel for autoinflammation and vasculitis (English) Ebun Omoyinmi
119 PP-55 Deficiency of Complement Component 1, r subcomponent presents as early onset SLE (English) Natalie Deuitch
140 PP-56 A rare case of ADAM17-related disease with a distinct phenotype (English) Sonia Melo Gomes
143 PP-57 TREX-1 mutation in the members of a family with Systemic Lupus Erythematosus and Antiphospholipid Syndrome (English) Serdal Ugurlu
149 PP-58 NEXT GENERATION SEQUENCING-BASED PANEL SCREENING IN PATIENTS WITH UNDIFFERENTIATED AUTOINFLAMMATORY DISEASES (English) Riccardo Papa
157 PP-59 AA amyloidosis related to familial mediterranean fever in France: a cohort study of 38 cases. (English) Georgin-Lavialle Sophie
183 PP-60 Canakinumab for Autoinflammatory Disease in Brazil (English) Leonardo Oliveira Mendonca
184 PP-61 Chronic recurrent multifocal osteomyelitis (CRMO): effect of neridronate. (English) Francesca Orlando
194 PP-62 CLINICAL RESPONSE TO USTEKINUMAB IN ERYTRODERMIC PSORIASIS CAUSED BY CARD14 MUTATION (CARD14 MEDIATED PSORIASIS;CAMPS)
 (English) Sara Signa
197 PP-63 Results of the Eurofever Delphi survey for the classification criteria for monogenic periodic fever syndromes (English) Silvia Federici
199 PP-64 Red Arthritis Helps To Distinguish Familial Mediterranean Fever From Other Rheumatic Conditions (English) Serdal Ugurlu
203 PP-65 Novel and de Novo PLCG2 Mutations in Two Patients with APLAID Syndrome (English) Juan Ignacio Arostegui
205 PP-66 Infection status in children with Familial Mediterranean fever (FMF) (English) Pelin Esmeray
207 PP-67 Targeted NGS study in 120 patients from Turkish population with autoinflammatory symptoms without MEFV gene mutations. (English) Afig berdeli
211 PP-68 Treatment of Familial Mediterranean Fever with Canakinumab in patients unresponsive to colchicine (English) Afig berdeli
234 PP-69 Anti-interleukin 1 Therapy in FMF Amyloidosis: a Single Center Experience (Case Series) (English) Serdal Ugurlu
235 PP-70 IL-1 Pathway Dysregulation in Periodic Fever, Aphthous Stomatitis, Pharyngitis, Adenitis (PFAPA) Syndrome (English) Lori Broderick
237 PP-71 Anakinra Treatment in Patients with Familial Mediterranean Fever: A Single-Center Experience (Case Series) (English) Serdal Ugurlu
240 PP-72 PFAPA syndrome among adults: a case series of 33 french cases (English) Georgin-Lavialle Sophie
246 PP-73 Recurrence of Proteinuria After Cessation of Tocilizumab in Patients with AA Amyloidosis Secondary To FMF (English) Sedat YILMAZ
247 PP-74 Recurrent Guillain-Barre Syndrome: A new autoinflammatory disease due to CD59 mutations (English) Dror Mevorach
103 PP-75 EVALUATION OF FIBROMYALGIA OCCURRENCE AND QUALITY OF LIFE IN PATIENTS WITH FAMILIAL MEDITERRANEAN FEVER (English) Kemal Erol
115 PP-76 IS CLINICAL SIGNIFICANCE OF MEFV R202Q IN FMF PATIENTS MORE THAN PREVIOUSLY EXPECTED? (English) Gülay Demircin
135 PP-77 Efficacy and safety of canakinumab in children with colchicine resistant or intolerant patients with FMF (English) Alper Soylu
137 PP-78 The Disease Burden of SJIA for Patients and Caregivers: An International HRQoL Survey and Retrospective Chart Review (English) Susan Shenoi
148 PP-79 Different disease severity in familial Mediterranean patients who had either M694V or M680I in both alleles (English) selcan demir
181 PP-80 Evaluation of Clinical Features, Genotype and Two Different Criteria for The Diagnosis of Familial Mediterranean Fever (English) Hulya Nalcacioglu
6 PP-81 JOINT SYNDROME AS THE PREDICTOR OF DEVELOPMENT OF AMYLOIDOSIS IN FAMILIAL MEDITERRANEAN FEVER. (English) Armine Simonyan
10 PP-82 Autoinflammatory and Autoimmunity Overlap: Familial Mediterranean Fever and ANA-Positive Chronic Anterior Uveitis (English) Basil Fathalla
13 PP-83 A CASE OF AMYLOIDOSIS CAUSED BY SPORADIC MUCKLE-WELLS SYNDROME: RESPONSE TO TREATMENT WITH ANAKINRA (English) Ufuk İlgen
15 PP-84 Successful treatment of anakinra in patient with familial Mediterranean fever related amyloidosis and nephrotic syndrome (English) NURVER AKINCI
17 PP-85 CNS manifestations of patients with Muckle-Wells syndrome (English) Sara Sebnem Kilic
21 PP-86 Genotype-phenotype correlation of patients with Familial Mediterranean Fever in childhood: experience of a single center (English) Miray Kisla Ekinci
26 PP-87 Clinical features and disease severity of Turkish children carrying E148Q mutation (English) fatma aydın
29 PP-88 Results of the Eurofever Delphi survey for the classification criteria of PFAPA syndrome (English) Federica Vanoni
39 PP-89 PRELIMINARY ANALYSIS OF 116 PATIENTS WITH CRONIC NON-BACTERIAL OSTEOMYELITIS (CNO) FROM THE EUROFEVER REGISTRY (English) Antonella Insalaco
41 PP-90 Deficiency of Adenosine Deaminase 2 Presenting with Amaurosis Fugax and Gastrointestinal Bleeding (English) Mustafa Çakan
42 PP-91 Efficacy of anti-IL-1 treatment in Familial Mediterranean Fever (English) Jeroen van der Hilst
43 PP-92 Three Cases of AA Amyloidosis Secondary to Familial Mediterranean Fever (English) Mustafa Çakan
45 PP-93 CHRONIC RECURRENT MULTIFOCAL OSTEOMYELITIS (CRMO) AND TUMORAL OSTEOLYTIC LESIONS: A SINGLE CENTRE EXPERIENCE (English) Martina Finetti
46 PP-94 Sustained Hyperferritinemia in a Child with Macrophage Activation Syndrome Secondary to sJIA: Chronic Perforinopathy (English) Mustafa Çakan
50 PP-95 Long-term monitorization of asymptomatic children heterozygous for MEFV mutation (English) Balahan Makay
60 PP-96 BEHÇET’S DISEASE IN CHILDREN (English) Ozge Başaran
65 PP-97 Clinical characteristics of familial Mediterranean fever patients according to their MEFV mutation (English) Pelin Esmeray
66 PP-98 Clinical Characteristics of FMF Patients According to Age Groups (English) Pelin Esmeray
67 PP-99 Re-introducing canakinumab treatment after macrophage activation syndrome (English) selcan demir
70 PP-100 Mutation-negative Familial Mediterranean Fever patients in childhood (English) ELİF ÇELİKEL
71 PP-101 Investigation of mannose-binding lectin gene polymorphisms in familial Mediterranean fever (English) Eren Erken
79 PP-102 CRONIC NON-BACTERIAL OSTEOMYELITIS (CNO) AND POLYARTERITIS NODOSA: A REPORT OF 2 CASES WITH AN UNUSUAL ASSOCIATION (English) Antonella Insalaco
80 PP-103 Natural course of mevalonic acid excretion and influence of pre-analytical sample handling of the patient with MKD (English) Sarka Fingerhutova
82 PP-104 VARIABLE CLINICAL PHENOTYPES AND RELATION OF INTERFERON SIGNATURE WITH DISEASE ACTIVITY IN ADA 2 DEFICIENCY (English) Antonella Insalaco
87 PP-105 Familial Mediterranean fever in Algeria- Results of three genetic studies (English) AIT-IDIR Djouher
96 PP-106 PFAPA syndrome – a qualitative study of parent’s experiences and strategies (English) Per Wekell
104 PP-107 MISDIAGNOSIS OF ACUTE RHEUMATIC FEVER IS NOT RARE IN PATIENTS WITH FAMILIAL MEDITERRANEAN FEVER (English) Kemal Erol
106 PP-108 A case of Familial Mediterranean Fever having intermittent leukopenia (English) İlke Beyitler
107 PP-109 ADENOSINE DEAMINASE 2 AND MEFV GENE MUTATION IN POLYARTERITIS NODOSA WITH A FATAL COURSE (English) Demet Alaygut
113 PP-110 Implementation of Next-Generation Sequencing for molecular genetic diagnostics of hereditary recurrent fever syndromes (English) Barbara Bangol
116 PP-111 Recurrent pericarditis in a child diagnosed as systemic – onset Juvenile Idiopathic Arthritis (English) İlke Beyitler
117 PP-112 A case of Familial Mediterranean Fever having intermittent leukopenia (English) İlke Beyitler
128 PP-113 Early Onset Sarcoidosis and Blau Syndrome: Six Patients Presentation (English) Zübeyde Gündüz
131 PP-114 THE ROLE OF MEFV MUTATIONS IN PFAPA SYNDROME (English) Gülay Demircin
134 PP-115 Results of azatiopurın in three patients with amyloidosis (English) Serpil Ergulu Esmen
141 PP-116 Atypical Varicella-Zoster Virus Infection in a Patient with Autoinflammatory Disease (English) Ines von Mühlenen
144 PP-117 Tocilizumab (anti-IL6) achieves complete and sustained remission in a patient with refractory CRMO (English) Erika Van Nieuwenhove
147 PP-118 HOIP mutations in a patient with CVID and autoinflammation (English) Hirotsugu Oda
150 PP-119 Autoinflammatory syndromes in a multisite consultation for pediatric immune-rheumatology: data from the JIRcohorte (English) Michaël Hofer
155 PP-120 THE MULTIFACETED PRESENTATION OF CHRONIC RECURRENT MULTIFOCAL OSTEOMYELITIS: 466 CASES FROM THE EUROFEVER REGISTRY (English) Martina Finetti
159 PP-121 Inflammatory Bowel Disease and Refractory Epilepsy responsive to anti-TNF therapy: an auto-inflammatory condition? (English) Leonardo Oliveira Mendonca
160 PP-122 From Patients to Doctors Side: FMF&AID, a non profit organization experience (English) Leonardo Oliveira Mendonca
164 PP-123 MEFV Genotype and Clinical Features of Familial Mediterranean Fever (FMF) in Cyprus (English) Jirayr Ajzajian
168 PP-124 Autoinflammation in a female carrier of NEMO (English) Fatma Dedeoglu
169 PP-125 Behcet’s disease in childhood: Single center ten years’ experience (English) DENİZ GEZGİN YILDIRIM
170 PP-126 Familial mediterranean fever (FMF) with spondyloarthritis in childhood (English) DENİZ GEZGİN YILDIRIM
171 PP-127 RENAL AMYLOIDOSIS SECONDARY TO FMF MASKED BY SHORT BOWEL SYNDROME: A CASE REPORT (English) Ruhan Dusunsel
172 PP-128 Uveitis case series; single center ten years’ experience, etiology and treatment regimens by subtypes (English) DENİZ GEZGİN YILDIRIM
175 PP-129 EVALUATION OF COGNITIVE FUNCTION ELECTROPHYSIOLOGICALLY IN CHILDREN WITH BEHÇET DISEASE (English) Nuray Aktay Ayaz
176 PP-130 We might have the same mutation but my inflammasome beats your inflammasome: CINCA versus FCAS (English) Mustafa Çakan
177 PP-131 Evaluation of Children with Behçet’s Disease from Regionally Two Different Centers of a Highly Prevalent Country

(English)

Nuray Aktay Ayaz
178 PP-132 HIDS patient presenting with immunodeficiency-like phenotype, recurrent pulmonary symptoms and persistent polyarthritis (English) Mustafa Çakan
182 PP-133 COEXISTENCE OF FAMILIAL MEDITERRANEAN FEVER, MUCOPOLYSACCHARIDOS TYPE 6 AND JUVENILE IDIOPATHIC ARTHRITIS: A CASE REPORT (English) Muammer Hakan Poyrazoglu
185 PP-134 Anhidrotic ectodermal dysplasia with autoinflammatory manifestations (English) Francesca Orlando
186 PP-135 Clinical picture of PFAPA syndrome in Ukrainian children (English) Yuriy Stepanovskyy
187 PP-136 Psoriasis in patients with familial Mediterranean fever (English) selcan demir
189 PP-137 The MEFV mutations and their clinical correlations in familial Mediterranean fever (English) özkan varan
190 PP-138 Novel mutation identified in severe early-onset tumor necrosis factor receptor-associated periodic syndrome (English) Lori Broderick
191 PP-139 Co-presenting Castleman’s disease and familial mediterranean fever leading to renal amyloidosis (English) zeynep erturk
192 PP-140 CLINICAL CHARACTERISTICS OF FAMILIAL MEDITERRANEAN FEVER PATIENTS WITH DELAY DIAGNOSIS (English) Hasmik Sargsyan
193 PP-141 A PRELIMINARY STUDY REGARDING TO THE LEVELS OF VITAMIN B12 AND FOLATE DURING COLCHICINE TREATMENT IN CHILDREN WITH FMF (English) Nuray Aktay Ayaz
195 PP-142 Use of whole-body magnetic resonance to identify potential diagnostic clues in children with fever of unknown origin (English) Sara Signa
198 PP-143 Measurement of the carotid intima media thickness (cIMT) of carotid arteries in pediatric Behçet’s Disease (English) Zehra Serap Arici
200 PP-144 Colchicine opocalcium treatment in Familial Mediterranean Fever in an infant. (English) Caner Alparslan
201 PP-145 Early diagnosis of an infant with ADA2 deficiency by resequencing of autoinflammatory disease panel by NGS. (English) Hiroshi Nihira
202 PP-146 Fatal Systemic Inflammation in Patients with Biallelic EGFR Mutations. A New Monogenic Autoinflammatory Disease? (English) Juan Ignacio Arostegui
206 PP-147 CXCL10 in CXCL9 genetic variants in children with Periodic fever with aphthous stomatitis, pharyngitis, and adenitis (English) Daša Perko
210 PP-148 Differential rate of Neutrophil Migration in Familial Mediterranean Fever Patients (English) Yeliz Z. Akkaya Ulum
213 PP-149 Impact of human monocyte and macrophage polarization on NLR expression and NLRP3 inflammasome activation (English) Fawaz Awad
215 PP-150 Scores and Outcome in Familial Mediterranean Fever (English) Maria Carrabba
216 PP-151 Neutrophil lymphocyte ratio in idiopathic uveitis and uveitis secondary to inflammatory/rheumatic conditions (English) DENİZ GEZGİN YILDIRIM
220 PP-152 Association of Disease Severity Score And Age of Disease Onset in Children with Familial Mediterranean Fever (English) Betül Öztürk
222 PP-153 Performance of the autoinflammatory disease damage index (ADDI) in patients with CAPS, TRAPS, HIDS and FMF (English) Jasmin Beate Kuemmerle-Deschner
223 PP-154 Tocilizumab treatment in two cases of AA amyloidosis complicated by familial Mediterranean fever (English) Serife Gul Karadag
224 PP-155 Juvenile arthritis caused by FAMIN (LACC1) mutations in two children with systemic and oligoarticular course (English) Anne Thorwarth
225 PP-156 COEXISTENCE OF FAMILIAL MEDITERRANEAN FEVER WITH MELKERSSON ROSENTHAL SYNDROME (CASE REPORT) (English) Hasmik Sargsyan
227 PP-157 Assessment And Following Up Of Chronic Disease Anemia In Patients With Familial Mediterranean Fever (English) Serife Gul Karadag
228 PP-158 Nutritionalstatus and risk factors in childrenwithFamilialMediterranean Fever (English) Zahide Ekici Tekin
229 PP-159 Compliance to colchicine treatment in Familial Mediterranean Fever related amyloidosis (English) Berna Yurttas
231 PP-160 The treatment responses of canakinumab in pediatric FMF patients (English) Fatma Yazılıtaş
233 PP-161 Evaluation of growth status in children with Familial Mediterranean fever (English) gulcin otar yener
242 PP-162 Case report of a patient with uncharacterized IFN-γ mediated autoinflammatory disorder (English) Oskar Schnappauf
243 PP-163 Papulopustular Lesions Differences in Behçet’s Syndrome Patients Compared to Healthy and Diseased Controls (English) Yesim Ozguler
244 PP-164 Liver abnormalities in adult patients with familial Mediterranean fever: a prospective study on metabolic features. (English) Georgin-Lavialle Sophie
248 PP-165 FDA Incentives for Drug Companies Make Colchicine Inaccessible to FMF Patients in the US (English) Janine Jagger
250 PP-166 Haplotype Analysis of Common MEFV Variants in Turkey (English) Kıvanç Bilecen
252 PP-167 Cutaneos Manifestation of Autoinflammatory Disease: Literature Review (English) Leonardo Oliveira Mendonca
105 PP-168 Osteitis as a non-canonical manifestation of Familial Mediterranean Fever (FMF) (English) Hakan Babaoğlu
158 PP-169 Spondyloarthritis associated with Familial Mediterranean fever: a case serie of 15 patients. (English) Georgin-Lavialle Sophie
31 PP-170 SUCCESSFUL TREATMENT OF STEROID-RESISTANT PROTRACTED FEBRILE MYALGIA SYNDROME WITH ANAKINRA: A CASE REPORT (English) Serife Gul Karadag
47 PP-171 Use of Canakinumab in Patient with Tumor Necrosis Factor Receptor-Associated Periodic Syndrome (TRAPS): A Case Report (English) Ayten Yazici
49 PP-172 Two Cases of Periodic Fever Syndrome with Coexistent MVK and MEFV gene Mutations (English) Mustafa Çakan
52 PP-173 ATYPICAL PRESENTATION OF FMF: ASCITES AND INTESTINAL OBSTRUCTION (English) Fatma Demirbaş
57 PP-174 Familial Mediterranean Fever-associated Coxofemoral arthritis: A Dramatic Responce to Anakinra (English) Hamit Kucuk
110 PP-175 Treatment of MKD with MEFV Mutation: Timing for Anti Interleukin-1 (English) Ceyhun Acari
121 PP-176 Chronic Recurrent Asseptic Meningitis and Hear Loss treated with Anti-IL6 therapy: case report and review of literature (English) Leonardo Oliveira Mendonca
122 PP-177 Novel compound heterozygous mutation in a Deficiency of Interleukin One Receptor Antagonist (DIRA) Brazilian patient (English) Leonardo Oliveira Mendonca
163 PP-178 Two cases of AA amyloidosis complicating HIDS diagnosed at the UK National Amyloidosis Centre (English) Dorota Rowczenio
173 PP-179 OUR CLINICAL EXPERIENCE IN THE PERIODIC FEVER, APHTHOUS STOMATITIS, PHARYNGITIS AND CERVICAL ADENITIS (PFAPA) SYNDROME (English) Nihal Sahin
188 PP-180 The Canacinumab Experience in a patient diagnosed with Familial Mediterranean Fever on Chronic Peritonial Dialysis (English) Eren Soyaltın
89 PP-181 Co-occurance of Atypical Onset Sacroiliitis and Familial Mediterranean Fever. A case Report. (English) Ozge Altug-Gucenmez
23 PP-182 Hyperimmunoglobulin D Syndrome: 3 Cases (English) Sibel Balci
136 PP-183 A Case of Hyperimmunglobulin D Syndrome Treated Successfully with Canakinumab (English) AYSE CEFLE